Darier's disease

From dermoscopedia

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 Authored by: Sabine Ludwig     ·  Aimilios Lallas

 Keywords:   darier's disease · darier
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Description This chapter describes dermoscopyDermoscopy is a non invasive diagnostic method. of dariers disease
Author(s) Sabine Ludwig · Aimilios Lallas
Owner Aimilios Lallas→ send e-mail
Status released
Status update July 11, 2017
Status by Ralph P. Braun
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Darieris an autosomal dominant disorder discovered by French dermatologist Ferdinand-Jean Darier. Darier's is characterized by dark crusty patches on the skin, sometimes containing pus. The crusty patches are also known as keratotic papules, keratosis follicularis or dyskeratosis follicularis.[4][5]

Mild forms of the disease are the most common, consisting solely of skin rashes that flare up under certain conditions such as high humidity, high stress or tight-fitting clothes. Even in mild forms, short stature combined with poorly formed fingernails containing vertical striations are diagnostic.’s disease

In Darier’s disease, dermoscopical analysis highlights the characteristic pseudocomedones and therefore is an effective additional tool for its clinical recognition. Vascular patterns are unspecific, comprising erythema, dotted and linear vesselsLinear mildly curved vessels considered irregular when different sizes shapes and curves with a haphazard or random distribution are presented and considered regular when short and fine (thin) linear vessels prevail various diagnoses.[1]
  1. Vázquez-López et al.: The handheld dermoscope improves the recognition of giant pseudocomedones in Darier's disease. J. Am. Acad. Dermatol. 2004;50:454-5. PMID: 14988691. DOI.